Evidence map›Paper›PMID 42516678›Full record

ArticlePulmonary circulation2026

Effectiveness of PAH Specific Treatment Is Comparable Between PAH Associated With Connective Tissue Disease and Idiopathic PAH: Data From the Multicentre National Registry.

Anna Smukowska-Gorynia, Sylwia Iwańczyk, Michał Ciurzyński, Marcin Waligóra, Marcin Kurzyna, Piotr Pruszczyk, Grzegorz Kopeć, Katarzyna Mizia-Stec, Ilona Skoczylas, Łukasz Chrzanowski and 17 more

Abstract read
In one paragraph

Article in Pulmonary circulation, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

0numbers the graph read from it
0cells of the map it votes in
0citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

0 citing papers in PubMed.

No citing paper in PubMed yet.

4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

27 authors.

Anna Smukowska-GoryniaDepartment of Cardiology Poznan University of Medical Sciences Poznań Poland.
Sylwia IwańczykDepartment of Cardiology Poznan University of Medical Sciences Poznań Poland.ORCID https://orcid.org/0000-0003-0509-6075
Michał CiurzyńskiDepartment of Internal Medicine and Cardiology With the Center for Diagnosis and Treatment of Venous Thromboembolism Medical University of Warsaw Warsaw Poland.
Marcin WaligóraDepartment of Cardiac and Vascular Diseases, John Paul II Hospital in KrCakow, 31-202 Krakow, Poland; Pulmonary Circulation Centre, Department of Cardiac and Vascular Diseases, Faculty of Medicine Jagiellonian University Medical College Krakow Poland.
Marcin KurzynaDepartment of Pulmonary Circulation, Thromboembolic Diseases and Cardiology Centre of Postgraduate Medical Education, European Health Centre Otwock Otwock Poland.ORCID https://orcid.org/0000-0002-6746-469X
Piotr PruszczykDepartment of Internal Medicine and Cardiology With the Center for Diagnosis and Treatment of Venous Thromboembolism Medical University of Warsaw Warsaw Poland.
Grzegorz KopećDepartment of Cardiac and Vascular Diseases, John Paul II Hospital in KrCakow, 31-202 Krakow, Poland; Pulmonary Circulation Centre, Department of Cardiac and Vascular Diseases, Faculty of Medicine Jagiellonian University Medical College Krakow Poland.
Katarzyna Mizia-StecFirst Department of Cardiology, I Chair of Cardiology Medical University of Silesia Katowice Poland.ORCID https://orcid.org/0000-0001-6907-2799
Ilona SkoczylasDepartment of Cardiology Faculty of Medical Sciences in Zabrze, Medical University of Silesia Katowice Poland.
Łukasz ChrzanowskiCardiology Department Medical University of Lodz Lodz Poland.
Piotr BłaszczakDepartment of Cardiology Cardinal Wyszynski Hospital Lublin Poland.
Katarzyna PtaszyńskaDepartment of Cardiology Medical University of Bialystok Bialystok Poland.
Grzegorz GrześkDepartment of Cardiology and Clinical Pharmacology Collegium Medicum in Bydgoszcz, Nicolaus Copernicus University in Toruń Toruń Poland.ORCID https://orcid.org/0000-0001-6669-5931
Ewa MalinowskaPulmonary Department University of Warmia and Mazury Olsztyn Poland.
Małgorzata Peregud-PogorzelskaDepartment of Cardiology Pomeranian Medical University Szczecin Poland.
Michał TomaszewskiDepartment of Cardiology Medical University of Lublin Lublin Poland.
Ewa MroczekDepartment of Cardiology Institute of Heart Diseases, Wroclaw Medical University Wroclaw Poland.
Miłosz JaguszewskiDepartment of Cardiology Medical University of Gdansk Gdansk Poland.
Ewa LewickaDepartment of Cardiology and Electrotherapy Medical University of Gdansk Gdansk Poland.
Katarzyna WidejkoDepartment of Cardiology Copper Health Center Lubin Poland.
Agnieszka PawlakDepartment of Invasive Cardiology, Polish Academy of Sciences, Mossakowski Medical Research Centre Central Clinical Hospital of the Ministry of Interior Warsaw Poland.
Wojciech JachećDepartment of Cardiology Faculty of Medical Sciences in Zabrze, Silesian Medical University in Katowice Zabrze Poland.
Zbigniew GąsiorDepartment of Cardiology School of Health Sciences in Katowice, Medical University of Silesia in Katowice Katowice Poland.
Katarzyna Betkier-LipińskaDepartment of Cardiology and Internal Medicine Military Institute of Medicine-National Research Institute Warsaw Poland.
Judyta Winowska-JózwaDepartment of Cardiology Samodzielny Publiczny Wojewódzki Szpital Zespolony Szczecin Poland.
Marta BanaszkiewiczDepartment of Pulmonary Circulation, Thromboembolic Diseases and Cardiology Centre of Postgraduate Medical Education, European Health Centre Otwock Otwock Poland.
Tatiana Mularek-KubzdelaDepartment of Cardiology Poznan University of Medical Sciences Poznań Poland.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Pulmonary arterial hypertension (PAH) is a rare disease with poor prognosis. The same treatment is recommended in patients with PAH associated with connective tissue disease (CTD) and idiopathic PAH (IPAH). However, the effectiveness of PAH-specific treatment in these both groups is inconsistent. The study incorporated data from the prospective, multicentre polish registry (BNP-PL) by comparison of baseline versus 1-year follow-up clinical, laboratory, echocardiographic and hemodynamic parameters in PAH-CTD versus IPAH group. The all-cause 1-year mortality was also analysed. 624 patients were included in the study: 176 (28%) PAH-CTD and 448 (72%) IPAH. 48 (8% of the total 624) patients died during 1-year follow up: 32 (7%) with IPAH and 16 (9%) with PAH-CTD (

Indexed as

comparison of IPAH and PAH‐CTDIPAHPAH‐CTDPAH‐specific therapyregistry

Identifiers

PMID42516678
PMCPMC13404781

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.