Evidence map›Paper›PMID 41535032›Full record

ArticleInternal medicine (Tokyo, Japan)2026

Sporadic Late-onset Nemaline Myopathy Presenting with Dropped Head Syndrome and Complicated with Sjögren's Syndrome.

Ayaka Seki, Tomonari Seki, Yuki Nagasako, Yusuke Sugiyama, Taro Bannai, Minako Yamada, Meiko Maeda, Akatsuki Kubota, Yasushi Shiio

Abstract readCase Reports
PubMed Full text at PMC Publisher
In one paragraph

Article in Internal medicine (Tokyo, Japan), 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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0citing papers in PubMed
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1 · What the graph read from it

What it found

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2 · The registry

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3 · Its place in the literature

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0 citing papers in PubMed.

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4 · The record

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5 · Who and what money

Authors and funding

9 authors.

Ayaka SekiDepartment of Neurology, Tokyo Teishin Hospital, Japan.
Tomonari SekiDepartment of Neurology, Tokyo Teishin Hospital, Japan.
Yuki NagasakoDepartment of Neurology, Tokyo Teishin Hospital, Japan.
Yusuke SugiyamaDepartment of Neurology, Tokyo Teishin Hospital, Japan.
Taro BannaiDepartment of Neurology, Tokyo Teishin Hospital, Japan.
Minako YamadaDepartment of Neurology, Tokyo Teishin Hospital, Japan.
Meiko MaedaDepartment of Neurology, The University of Tokyo, Japan.
Akatsuki KubotaDepartment of Neurology, The University of Tokyo, Japan.
Yasushi ShiioDepartment of Neurology, Tokyo Teishin Hospital, Japan.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Sporadic late-onset nemaline myopathy (SLONM) is a rare neuromuscular disorder often associated with monoclonal gammopathy of undetermined significance (MGUS). However, reports of SLONM without MGUS are limited, particularly in cases complicated by Sjögren's syndrome. We herein report the case of a 62-year-old woman with SLONM without MGUS, associated with Sjögren's syndrome. The patient presented with dropped head syndrome. A muscle biopsy confirmed SLONM, and Sjögren's syndrome was diagnosed. Treatment with intravenous immunoglobulin and corticosteroids improved her muscle strength. This case highlights the importance of considering SLONM in the differential diagnosis when dropped head is the predominant clinical presentation.

Indexed as

Dropped Head SyndromeMyopathies, NemalineSjogren's SyndromeDiagnosis, DifferentialFemaleHumansImmunoglobulins, IntravenousMiddle AgedMuscle, SkeletalImmunoglobulins, IntravenousSjögren's syndromeSLONM

Identifiers

PMID41535032
PMCPMC13561564

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