Hepatopulmonary syndrome from liver disease associated with autosomal recessive polycystic kidney disease.

Alexander Cowcher, Joshua Kausman, Simon Carter, Winita Hardika, Joanne Harrison, Sheena Kaul, Bennett Sheridan, Thomas Forbes, Catherine Quinlan

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In one paragraph

Article in Pediatric nephrology (Berlin, Germany), 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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5 · Who and what money

Authors and funding

9 authors.

Alexander CowcherThe Royal Children's Hospital, Melbourne, Australia.

Joshua KausmanDepartment of Paediatric Nephrology, The Royal Children's Hospital, Melbourne, Australia.

Simon CarterDepartment of Paediatric Nephrology, The Royal Children's Hospital, Melbourne, Australia.

Winita HardikaDepartment of Liver and Intestinal Transplantation, The Royal Children's Hospital, Melbourne, Australia.

Joanne HarrisonThe Royal Children's Hospital, Melbourne, Australia.

Sheena KaulDepartment of Paediatric Nephrology, The Royal Children's Hospital, Melbourne, Australia.

Bennett SheridanDepartment of Cardiology, The Royal Children's Hospital, Melbourne, Australia.

Thomas ForbesDepartment of Paediatric Nephrology, The Royal Children's Hospital, Melbourne, Australia.

Catherine QuinlanDepartment of Paediatric Nephrology, The Royal Children's Hospital, Melbourne, Australia. cathy.quinlan@rch.org.au.ORCID http://orcid.org/0000-0003-2746-6903

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Hepatopulmonary syndrome (HPS) is a life-threatening complication of chronic liver disease (CLD) that currently can be managed only by liver transplant. Though uncommon, some children with kidney disease have coexistent CLD and hence are at risk of developing HPS. Paediatric cases of HPS are rarely described in the nephrology literature. We present a patient with autosomal recessive polycystic kidney disease (ARPKD) and persistent hypoxaemia diagnosed as HPS and successfully managed with a liver transplant. We suggest that nephrologists caring for children with kidney and concomitant CLD consider routine screening for HPS with pulse oximetry.

Indexed as

Hepatopulmonary SyndromeLiver DiseasesPolycystic Kidney, Autosomal RecessiveHumansLiver TransplantationTreatment OutcomeAutosomal recessive polycystic kidney diseaseChronic liver diseaseHepatopulmonary syndrome

Identifiers

PMID39832013

DOI10.1155/2017/2171974

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