Adrenal lymphangioma: Case report and review of the literature.

introduction and importanceLymphangiomas (LG) are a rare type of lesion of the lymphatic vessels. They predominantly occur in young patients, mostly female. Adrenal location represents 0.06 % of reported cases in the literature. Characteristically, LGs are often clinically silent and discovered incidentally during abdominal imaging studies performed for other reasons. Definitive diagnosis is done by the histopathologic analysis of the specimen. The rarity of this pathology and the lack of reports makes this entity challenging. CASE PRESENTATION: We present a 48-year-old man referred to our institution for a left adrenal solid mass incidentally discovered in CT abdominal scan (103 × 62 mm). CLINICAL DISCUSSION: Patient underwent laparoscopic surgical excision of the tumor. The histopathology examination showed the presence of cystic structures with fibrous walls and parietal calcifications. Immunohistochemical staining was positive for D2-40 and CD31. These findings were compatible with LG of the adrenal gland. We discuss adrenal lymphangioma as a rare differential diagnosis of adrenal cystic lesions.

conclusionAdrenal LGs are rare tumors and, despite some clues for radiologic diagnosis, preoperative diagnosis is challenging. In symptomatic patients or in cases where malignancy cannot be excluded, surgery is recommended. In general, the prognosis of LGs is excellent.