Evidence map›Paper›PMID 39444900›Full record

ReviewJournal of thoracic disease2024

Rare interstitial lung diseases: a narrative review.

Karina Portillo Carroz, Blanca Urrutia-Royo, Antonio Marin, Laura Rodriguez Pons, Paloma Millán-Billi, Antoni Rosell, Onofre Moran-Mendoza

Abstract readReview
In one paragraph

Review in Journal of thoracic disease, 2024. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 2 papers, 1 of them a synthesis that pooled it.

0numbers the graph read from it
0cells of the map it votes in
2citing papers in PubMed, 1 pooled it
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

2 citing papers in PubMed, 1 synthesis or guideline pooled it.

  1. Pooled it
  2. Review
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

7 authors.

Karina Portillo CarrozPulmonology Department, Hospital Universitari Germans Trias i Pujol, Badalona, Spain.ORCID https://orcid.org/0000-0002-7804-1051
Blanca Urrutia-RoyoPulmonology Department, Hospital Consortium of Maresme, Mataró, Spain.ORCID https://orcid.org/0000-0002-1978-2773
Antonio MarinPulmonology Department, Hospital Universitari Germans Trias i Pujol, Badalona, Spain.ORCID https://orcid.org/0000-0002-1749-4583
Laura Rodriguez PonsPulmonology Department, Hospital Universitari Germans Trias i Pujol, Badalona, Spain.ORCID https://orcid.org/0000-0003-2799-9937
Paloma Millán-BilliPulmonology Department, Hospital Universitari Germans Trias i Pujol, Badalona, Spain.ORCID https://orcid.org/0000-0003-4664-0516
Antoni RosellPulmonology Department, Hospital Universitari Germans Trias i Pujol, Badalona, Spain.ORCID https://orcid.org/0000-0003-0877-7191
Onofre Moran-MendozaDivision of Respirology and Sleep Medicine, Queen's University, Kingston, ON, Canada.ORCID https://orcid.org/0000-0002-7156-0481

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Background and Objective: Interstitial lung diseases (ILDs) encompass over 200 entities. Among them, fibrosing lung diseases, have recently generated special interest due to the emerging therapies for their management. However, it is important to deepen our knowledge of other less prevalent ILD, since many of them are associated with a poor prognosis. This narrative review aims to provide a practical and up-to-date description of some poorly recognized ILD. It covers rare idiopathic interstitial pneumonias and their histologic patterns, genetic disorders with interstitial lung involvement (Hermansky-Pudlak syndrome), and ILD associated with benign proliferation of pulmonary lymphoid tissue, namely follicular bronchiolitis and granulomatous-lymphocytic interstitial lung disease. Methods: Electronic searches of PubMed and Google Scholar using specific keywords were conducted. Articles underwent screening for relevance, covering review articles, meta-analyses, systematic reviews, case series, prospective studies, society guidelines, editorials in peer-reviewed journals; scientific books on the subject. The data included was limited to English and Spanish publications. Key Content and Findings: Despite the low prevalence of these diseases, the increased recognition of radiological patterns, pathological features, and diagnostic procedures, have permitted their better characterization. This review highlights epidemiology, clinical presentation, diagnosis, natural history, and treatment. Conclusions: Lesser-studied ILD represent a diagnostic and therapeutic challenge and can be frequently misdiagnosed. Also, due to the lack of randomized controlled trials, there are no well-established therapeutic options. Further studies or registries are needed to improve accurate diagnosis and management.

Indexed as

acute fibrinous organizing pneumonia (AFOP)granulomatous-lymphocytic interstitial lung disease (GLILD)Hermansky-Pudlak syndrome (HPS)Rare idiopathic interstitial pneumonias

Identifiers

PMID39444900
PMCPMC11494586

What OpenQuestion holds

Textmetadata
LicenceCC BY-NC-ND
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.