Evidence map›Paper›PMID 38302155›Full record

ArticleThe European respiratory journal2024

Cystic fibrosis in Europe: improved lung function and longevity - reasons for cautious optimism, but challenges remain.

Eitan Kerem, Annalisa Orenti, Arianna Adamoli, Elpis Hatziagorou, Lutz Naehrlich, Isabelle Sermet-Gaudelus, and the ECFS Patient Registry Steering Group

Abstract read
In one paragraph

Article in The European respiratory journal, 2024. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 24 papers.

0numbers the graph read from it
0cells of the map it votes in
24citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

24 citing papers in PubMed.

  1. Article
  2. Article
  3. Article
  4. Review
  5. Review
  6. Citrus Flavonoids for Cystic Fibrosis Treatment.Chembiochem : a European journal of chemical biology · 2025
    Review
  7. Chronic lung infection byRevista espanola de quimioterapia : publicacion oficial de la Sociedad Espanola de Quimioterapia · 2025
    Article
  8. Review
  9. Article
  10. Article
  11. Review
  12. OvercomingAntibiotics (Basel, Switzerland) · 2025
    Review
  13. 20 years of the Montreal Cystic Fibrosis Related Diabetes Screening Cohort: key insights.European respiratory review : an official journal of the European Respiratory Society · 2025
    Review
  14. Article
  15. Review
  16. Article
  17. Article
  18. Review
  19. The ageing of people living with cystic fibrosis: what to expect now?European respiratory review : an official journal of the European Respiratory Society · 2024
    Review
  20. Cystic fibrosis.Nature reviews. Disease primers · 2024
    Review
4 · The record

Corrections and comments

5 · Who and what money

Authors and funding

7 authors.

Eitan KeremDepartment of Paediatrics and CF Centre, Hebrew University Medical School, Hadassah Medical Center, Jerusalem, Israel kerem@hadassah.org.il.ORCID https://orcid.org/0000-0002-4635-386X
Annalisa OrentiDepartment of Clinical Sciences and Community Health, Laboratory of Medical Statistics, Biometry and Epidemiology "G.A. Maccaccaro", University of Milan, Milan, Italy.ORCID https://orcid.org/0000-0002-0932-2757
Arianna AdamoliDepartment of Clinical Sciences and Community Health, Laboratory of Medical Statistics, Biometry and Epidemiology "G.A. Maccaccaro", University of Milan, Milan, Italy.
Elpis HatziagorouPaediatric Pulmonology and Cystic Fibrosis Unit, 3rd Paediatric Department, Hippokration Hospital, Aristotle University of Thessaloniki, Thessaloniki, Greece.ORCID https://orcid.org/0000-0001-9505-2054
Lutz NaehrlichDepartment of Pediatrics, Justus Liebig University Giessen, Giessen, Germany.
Isabelle Sermet-GaudelusCystic Fibrosis National Pediatric Reference Center, Pneumo-Allergologie Pédiatrique, Hôpital Necker Enfants Malades, AP-HP, Paris, France.ORCID https://orcid.org/0000-0001-5537-9482
and the ECFS Patient Registry Steering Group

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

backgroundPrognosis and disease severity in cystic fibrosis (CF) are linked to declining lung function. To characterise lung function by the number of adults in countries with different levels of Gross National Income (GNI), data from the European Cystic Fibrosis Society Patient Registry were utilised.

methodsAnnual data including age, forced expiratory volume in 1 s (FEV

resultsA consistent improvement in FEV

conclusionThis pan-European analysis demonstrates a consistent improvement in FEV

Indexed as

Cystic FibrosisAdultChildCystic Fibrosis Transmembrane Conductance RegulatorEuropeHumansLongevityLungMutationCystic Fibrosis Transmembrane Conductance Regulator

Identifiers

PMID38302155
PMCPMC10918317

What OpenQuestion holds

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Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.