Evidence map›Paper›PMID 37547321›Full record

ArticleFrontiers in endocrinology2023

Anticipated effects of burosumab treatment on long-term clinical sequelae in XLH: expert perspectives.

Lothar Seefried, Martin Biosse Duplan, Karine Briot, Michael T Collins, Rachel Evans, Pablo Florenzano, Neil Hawkins, Muhammad Kassim Javaid, Robin Lachmann, Leanne M Ward

Abstract read
In one paragraph

Article in Frontiers in endocrinology, 2023. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 14 papers.

0numbers the graph read from it
0cells of the map it votes in
14citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

14 citing papers in PubMed.

  1. Article
  2. Article
  3. Article
  4. Article
  5. Article
  6. Article
  7. Review
  8. Article
  9. Article
  10. Article
  11. Review
  12. Article
  13. Rare genetic skeletal disorders: Evolving terminology, therapies, education and advocacy.Journal of the Pediatric Orthopaedic Society of North America · 2024
    Article
  14. Novel therapies for growth disorders.European journal of pediatrics · 2024
    Review
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

10 authors.

Lothar SeefriedOrthopedic Department, University of Würzburg, Würzburg, Germany.
Martin Biosse DuplanService de Médecine Bucco-Dentaire, Hôpital Bretonneau, AP-HP, Paris, France.
Karine BriotDepartment of Rheumatology, Hôpital Cochin, Université de Paris-Cité, Paris, France.
Michael T CollinsSkeletal Disorders and Mineral Homeostasis Section, National Institutes of Dental and Craniofacial Research, National Institutes of Health, Bethesda, MD, United States.
Rachel EvansHealth Economics, Visible Analytics, Oxford, United Kingdom.
Pablo FlorenzanoDepartment of Endocrinology, Pontificia Universidad Católica de Chile, Santiago, Chile.
Neil HawkinsHealth Economics, Visible Analytics, Oxford, United Kingdom.
Muhammad Kassim JavaidNuffield Department of Orthopaedics, Rheumatology and Musculoskeletal Sciences, University of Oxford, Oxford, United Kingdom.
Robin LachmannCharles Dent Metabolic Unit, National Hospital for Neurology and Neurosurgery, London, United Kingdom.
Leanne M WardChildren's Hospital of Eastern Ontario, University of Ottawa, Ottawa, ON, Canada.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

X-linked hypophosphatemia (XLH) is a rare, progressive, genetic disease with multisystem impact that typically begins to manifest in early childhood. Two treatment options exist: oral phosphate in combination with active vitamin D ("conventional therapy") and a fully human monoclonal anti-FGF23 antibody, burosumab. The clinical benefit of conventional therapy in adults is limited, and poor tolerance and complications are common. Burosumab was first approved as a treatment for XLH in 2018 and its disease-modifying benefits in clinical trials in children suggest burosumab treatment could also alter the disease course in adults. Without long-term clinical data on multiple XLH-related sequelae available, the results of an elicitation exercise are reported, in which eight global experts in XLH posited how long-term treatment with burosumab is anticipated to impact the life course of clinical sequelae in adults with XLH. Based on their clinical experiences, the available evidence and their disease understanding, the experts agreed that some long-term benefits of using burosumab are likely in adults with XLH even if they have a misaligned skeleton from childhood. Burosumab treatment is anticipated to reduce the incidence of fractures and halt the progression of clinical sequelae associated with conventional therapy. While the trajectories for established dental abscesses are not expected to improve with burosumab treatment, dental abscess development may be prevented. Starting treatment with burosumab in childhood to increase the likelihood of an aligned skeleton and continuation into and throughout adulthood to maintain euphosphatemia may optimize patient outcomes, although future real-world investigation is required to support this hypothesis.

Indexed as

Familial Hypophosphatemic RicketsAdultAntibodies, MonoclonalAntibodies, Monoclonal, HumanizedChildChild, PreschoolDisease ProgressionHumansPhosphatesRare DiseasesAntibodies, MonoclonalAntibodies, Monoclonal, HumanizedburosumabPhosphatesburosumabfibroblast growth factor 23hypophosphatemiaphosphate metabolismX-linked hypophosphatemia

Identifiers

PMID37547321
PMCPMC10400326

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Registered trials

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.