Evidence map›Paper›PMID 33552905›Full record

ArticleMolecular genetics and metabolism reports2021

Nutrient management in the intrapartum period in maternal maple syrup urine disease.

Chika Takano, Mika Ishige, Erika Ogawa, Nobuhiko Nagano, Tamaki Morohashi, Aya Okahashi, Kaori Kawakami, Atsushi Komatsu, Kei Kawana, Tatsuhiko Urakami and 1 more

Open access · goldAbstract readCase Reports
PubMed Full text at PMC Publisher
In one paragraph

Article in Molecular genetics and metabolism reports, 2021. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 1 paper.

0numbers the graph read from it
0cells of the map it votes in
1citing papers in PubMed
0.1field-weighted citation impact, top 56% of its field
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

1 citing paper in PubMed, 1 citations in OpenAlex.

  1. Review
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

11 authors at 1 institution in 1 country.

Chika TakanoDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Mika IshigeDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Erika OgawaDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Nobuhiko NaganoDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Tamaki MorohashiDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Aya OkahashiDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Kaori KawakamiDepartment of Obstetrics and Gynecology, Nihon University School of Medicine, Tokyo, Japan.
Atsushi KomatsuDepartment of Obstetrics and Gynecology, Nihon University School of Medicine, Tokyo, Japan.
Kei KawanaDepartment of Obstetrics and Gynecology, Nihon University School of Medicine, Tokyo, Japan.
Tatsuhiko UrakamiDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Ichiro MoriokaDepartment of Pediatrics and Child Health, Nihon University School of Medicine, Tokyo, Japan.
Nihon University · JP

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Women with congenital amino acid disorders, including maple syrup urine disease (MSUD), are at risk of metabolic crisis at delivery. There are still only a few case reports of maternal MSUD globally, and we are the first to report the successful perinatal management of a woman with classical MSUD in Japan. A healthy baby was delivered by scheduled cesarean section despite the presence of several uterine fibroids. With precise diet therapy and accurate preparation, she completed the postpartum period without metabolic decompensation. Although her clinical outcome was favorable, she experienced hypoproteinemia at delivery because the available branched-chain amino acid-free medical food did not contain sufficient protein to meet the recommended nutrient intake. Therefore, this case also indicates a potential issue regarding a shortage of variations in specific amino acid-free medical food in Japan, which should be addressed to achieve a better nutrient status of adults with MSUD and other amino acid disorders.

Indexed as

Diet therapyMaple syrup urine diseasePerinatal managementUterine fibroid

Identifiers

PMID33552905
PMCPMC7848629
OpenAlexW3127161715

What OpenQuestion holds

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LicenceCC BY-NC-ND
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Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.