Evidence map›Paper›PMID 33240484›Full record

ArticlePulmonary circulation

Peripheral pulmonary stenosis with Noonan syndrome treated by balloon pulmonary angioplasty.

Seien Ko, Jin Komuro, Yoshinori Katsumata, Yasuyuki Shiraishi, Takashi Kawakami, Yoshitake Yamada, Shinsuke Yuasa, Takashi Kohno, Kenjiro Kosaki, Keiichi Fukuda

Open access · goldAbstract readCase Reports
In one paragraph

Article in Pulmonary circulation. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 3 papers.

0numbers the graph read from it
0cells of the map it votes in
3citing papers in PubMed
0.5field-weighted citation impact, top 37% of its field
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

3 citing papers in PubMed, 7 citations in OpenAlex.

  1. Adult-onset idiopathic peripheral pulmonary artery stenosis.The European respiratory journal · 2023
    Article
  2. Review
  3. The treatment dilemma in adult patients with peripheral pulmonary artery stenosis of diverse etiologies.The Egyptian heart journal : (EHJ) : official bulletin of the Egyptian Society of Cardiology · 2021
    Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

10 authors at 1 institution in 1 country.

Seien KoDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Jin KomuroDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Yoshinori KatsumataDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Yasuyuki ShiraishiDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Takashi KawakamiDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Yoshitake YamadaDepartment of Radiology, Keio University School of Medicine, Tokyo, Japan.
Shinsuke YuasaDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Takashi KohnoDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Kenjiro KosakiDivision of Medical Genetics Department of Pediatrics, Keio University School of Medicine, Tokyo, Japan.
Keiichi FukudaDepartment of Cardiology, Keio University School of Medicine, Tokyo, Japan.
Keio University · JP

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Noonan syndrome is known to have various cardiovascular defects, which include pulmonary artery stenosis. Pulmonary artery stenosis is characterized by obstruction of pulmonary artery blood flow that can cause elevated pulmonary artery pressure and ventilation-perfusion inequality, which can cause dyspnea on exertion and eventually, heart failure. Although the etiology of pulmonary artery stenosis related to congenital diseases is still unknown, balloon pulmonary angioplasty has being reported to be effective to selected patients with Alagille and Williams syndromes, but not from Noonan syndrome despite of modest prevalence of pulmonary artery stenosis. Here, we report the first Noonan syndrome patient with pulmonary artery stenosis who underwent successful balloon pulmonary angioplasty. The strategy used in balloon pulmonary angioplasty was planned with careful morphologic evaluation by computed tomographic angiography, and performed with scoring balloons in a graded approach with multiple sessions. After balloon pulmonary angioplasty, we confirmed maintained dilation of lesions and symptom alleviation, suggesting that balloon pulmonary angioplasty can be performed safely on pulmonary artery stenosis in a Noonan syndrome patient.

Indexed as

catheter interventionpulmonary hypertensionventilation perfusion ratio inequality

Identifiers

PMID33240484
PMCPMC7675873
OpenAlexW3092484131

What OpenQuestion holds

Textmetadata
LicenceCC BY-NC
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.