Evidence map›Paper›PMID 31899609›Full record

ArticleMolecular genetics & genomic medicine2020

Developmental aspects of FXAND in a man with the FMR1 premutation.

Ellery Santos, Chinelo Emeka-Nwonovo, Jun Yi Wang, Andrea Schneider, Flora Tassone, Paul Hagerman, Randi Hagerman

Open access · goldAbstract readCase Reports
In one paragraph

Article in Molecular genetics & genomic medicine, 2020. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 4 papers.

0numbers the graph read from it
0cells of the map it votes in
4citing papers in PubMed
0.7field-weighted citation impact, top 27% of its field
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

4 citing papers in PubMed, 5 citations in OpenAlex.

  1. Review
  2. Evidence for Three Subgroups of FemaleFrontiers in integrative neuroscience · 2021
    Article
  3. Article
  4. Developmental aspects of FXAND in a man with the FMR1 premutation.Molecular genetics & genomic medicine · 2020
    Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

7 authors at 2 institutions in 1 country.

Ellery SantosMIND Institute, University of California Davis School of Medicine, Sacramento, CA, USA.ORCID 0000-0001-6301-7262
Chinelo Emeka-NwonovoMIND Institute, University of California Davis School of Medicine, Sacramento, CA, USA.
Jun Yi WangMIND Institute, University of California Davis School of Medicine, Sacramento, CA, USA.
Andrea SchneiderMIND Institute, University of California Davis School of Medicine, Sacramento, CA, USA.ORCID 0000-0002-4674-7244
Flora TassoneMIND Institute, University of California Davis School of Medicine, Sacramento, CA, USA.
Paul HagermanMIND Institute, University of California Davis School of Medicine, Sacramento, CA, USA.
Randi HagermanMIND Institute, University of California Davis School of Medicine, Sacramento, CA, USA.ORCID 0000-0001-5029-8448
University of California, Davis · USUniversity of California Davis Medical Center · US

Funding

GENOTYPE/PHENOTYPE RELATIONSHIPS IN FRAGILE X FAMILIESR01HD036071 · NICHD · UNIVERSITY OF CALIFORNIA DAVIS · PI PAUL J HAGERMAN, RANDI J. HAGERMAN · 1998 to 2026
$13.8M
Research Project: Pathologic Significance of Maternal AutoantibodiesP50HD103526 · NICHD · UNIVERSITY OF CALIFORNIA AT DAVIS · PI LEONARD J. ABBEDUTO, Melissa Dawn Bauman · 2020 to 2026
$9.7M
Rodent Behavior CoreU54HD079125 · NICHD · UNIVERSITY OF CALIFORNIA AT DAVIS · PI SIMON, TONY J · 2013 to 2019
$8.5M
NICHD NIH HHS P50 HD103526NICHD NIH HHS R01 HD036071NICHD NIH HHS U54 HD079125
6 · The paper itself

Abstract

backgroundFragile X mental retardation 1 (FMR1) premutation can cause developmental problems including autism spectrum disorder (ASD), social anxiety, depression, and attention deficit hyperactivity disorder (ADHD). These problems fall under an umbrella term of Fragile X-associated Neuropsychiatric Disorders (FXAND) and is separate from Fragile X-associated Tremor/Ataxia syndrome (FXTAS), a neurodegenerative disorder. METHODS/CLINICAL CASE: A 26-year-old Caucasian male with the Fragile X premutation who presented with multiple behavior and emotional problems including depression and anxiety at 10 years of age. He was evaluated at 13, 18, and 26 years old with age-appropriate cognitive assessments, psychiatric evaluations, and an MRI of the brain.

resultsThe Autism Diagnostic Observation Scale (ADOS) was done at 13 years old and showed the patient has autism spectrum disorder (ASD). An evaluation at 18 years old showed a full-scale IQ of 64. A Kiddie Schedule for Affective Disorders and Schizophrenia (K-SADS) performed at 26 years old confirmed the previous impression of social anxiety disorder, agoraphobia disorder, and selective mutism. His MRI acquired at 26 years old showed enlarged ventricles, increased frontal subarachnoid spaces, and hypergyrification.

conclusionThis is an exemplary case of an FMR1 premutation carrier with significant psychiatric and cognitive issues that demonstrates Fragile X-associated Neuropsychiatric Disorders (FXAND) as separate from the other well-known premutation disorders.

Indexed as

PhenotypeAdultBrainCognitionFragile X Messenger Ribonucleoprotein 1Fragile X SyndromeHumansMagnetic Resonance ImagingMalePsychiatric Status Rating ScalesFMR1 protein, humanFragile X Messenger Ribonucleoprotein 1ASDFMR1Fragile XFXANDPremutation

Identifiers

PMID31899609
PMCPMC7005639
OpenAlexW2997304171

What OpenQuestion holds

Textmetadata
LicenceCC BY
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.