Evidence map›Paper›PMID 31379802›Full record

ArticleFrontiers in immunology2019

The German National Registry of Primary Immunodeficiencies (2012-2017).

Sabine M El-Helou, Anika-Kerstin Biegner, Sebastian Bode, Stephan R Ehl, Maximilian Heeg, Maria E Maccari, Henrike Ritterbusch, Carsten Speckmann, Stephan Rusch, Raphael Scheible and 140 more

Abstract read
In one paragraph

Article in Frontiers in immunology, 2019. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 49 papers, 2 of them syntheses that pooled it.

0numbers the graph read from it
0cells of the map it votes in
49citing papers in PubMed, 2 pooled it
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

49 citing papers in PubMed, 2 syntheses or guidelines pooled it.

  1. Pooled it
  2. Pooled it
  3. Trial
  4. Trial
  5. Observational
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  20. Phenotypic presentation of Mendelian disease across the diagnostic trajectory in electronic health records.Genetics in medicine : official journal of the American College of Medical Genetics · 2023
    Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

150 authors.

Sabine M El-HelouInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Anika-Kerstin BiegnerInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Sebastian BodeInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Stephan R EhlInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Maximilian HeegInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Maria E MaccariInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Henrike RitterbuschInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Carsten SpeckmannCenter for Pediatrics and Adolescent Medicine, Medical Center, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Stephan RuschInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Raphael ScheibleInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Klaus WarnatzDepartment of Rheumatology and Clinical Immunology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Faranaz AtschekzeiDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Renata BeiderDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Diana ErnstDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Stev GerschmannDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Alexandra JablonkaDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Gudrun MielkeDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Reinhold E SchmidtDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Gesine SchürmannDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Georgios SogkasDepartment of Clinical Immunology and Rheumatology, Hannover Medical School, Hannover, Germany.
Ulrich H BaumannDepartment of Paediatric Pulmonology, Allergy and Neonatology, Hannover Medical School, Hannover, Germany.
Christian KlemannDepartment of Paediatric Pulmonology, Allergy and Neonatology, Hannover Medical School, Hannover, Germany.
Dorothee ViemannDepartment of Paediatric Pulmonology, Allergy and Neonatology, Hannover Medical School, Hannover, Germany.
Horst von BernuthDepartment of Pediatric Pneumology, Immunology and Intensive Care, Charité - Universitätsmedizin Berlin, Berlin, Germany.
Renate KrügerDepartment of Pediatric Pneumology, Immunology and Intensive Care, Charité - Universitätsmedizin Berlin, Berlin, Germany.
Leif G HanitschOutpatient Clinic for Immunodeficiencies, Institute Medical Immunology, Charité - Universitätsmedizin Berlin, Berlin, Germany.
Carmen M ScheibenbogenOutpatient Clinic for Immunodeficiencies, Institute Medical Immunology, Charité - Universitätsmedizin Berlin, Berlin, Germany.
Kirsten WittkeOutpatient Clinic for Immunodeficiencies, Institute Medical Immunology, Charité - Universitätsmedizin Berlin, Berlin, Germany.
Michael H AlbertDepartment of Pediatrics, Dr. von Hauner Children's Hospital, University Hospital, Ludwig-Maximilians-University Munich, Munich, Germany.
Anna EichingerDepartment of Pediatrics, Dr. von Hauner Children's Hospital, University Hospital, Ludwig-Maximilians-University Munich, Munich, Germany.
Fabian HauckDepartment of Pediatrics, Dr. von Hauner Children's Hospital, University Hospital, Ludwig-Maximilians-University Munich, Munich, Germany.
Christoph KleinDepartment of Pediatrics, Dr. von Hauner Children's Hospital, University Hospital, Ludwig-Maximilians-University Munich, Munich, Germany.
Anita Rack-HochDepartment of Pediatrics, Dr. von Hauner Children's Hospital, University Hospital, Ludwig-Maximilians-University Munich, Munich, Germany.
Franz M SollingerDepartment of Pediatrics, Dr. von Hauner Children's Hospital, University Hospital, Ludwig-Maximilians-University Munich, Munich, Germany.
Anne AvilaImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Michael BorteImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Stephan BorteImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Maria FasshauerImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Anja HauenhermImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Nils KellnerImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Anna H MüllerImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Anett ÜlzenImmunoDeficiencyCenter Leipzig (IDCL), Hospital St. Georg gGmbH Leipzig, Academic Teaching Hospital of the University of Leipzig, Leipzig, Germany.
Peter BaderDivision for Stem Cell Transplantation and Immunology, Department for Children and Adolescents, Frankfurt University Hospital, Frankfurt, Germany.
Shahrzad BakhtiarDivision for Stem Cell Transplantation and Immunology, Department for Children and Adolescents, Frankfurt University Hospital, Frankfurt, Germany.
Jae-Yun LeeDivision for Stem Cell Transplantation and Immunology, Department for Children and Adolescents, Frankfurt University Hospital, Frankfurt, Germany.
Ursula HeßDepartment for Children and Adolescents, Division for Allergology, Pneumology and Cystic Fibrosis, University Hospital Goethe University, Frankfurt am Main, Germany.
Ralf SchubertDepartment for Children and Adolescents, Division for Allergology, Pneumology and Cystic Fibrosis, University Hospital Goethe University, Frankfurt am Main, Germany.
Sandra WölkeDepartment for Children and Adolescents, Division for Allergology, Pneumology and Cystic Fibrosis, University Hospital Goethe University, Frankfurt am Main, Germany.
Stefan ZielenDepartment for Children and Adolescents, Division for Allergology, Pneumology and Cystic Fibrosis, University Hospital Goethe University, Frankfurt am Main, Germany.
Sujal GhoshDepartment of Pediatric Oncology, Hematology and Clinical Immunology, Medical Faculty, University Children's Hospital, Heinrich-Heine-University, Düsseldorf, Germany.
Hans-Juergen LawsDepartment of Pediatric Oncology, Hematology and Clinical Immunology, Medical Faculty, University Children's Hospital, Heinrich-Heine-University, Düsseldorf, Germany.
Jennifer NeubertDepartment of Pediatric Oncology, Hematology and Clinical Immunology, Medical Faculty, University Children's Hospital, Heinrich-Heine-University, Düsseldorf, Germany.
Prasad T OommenDepartment of Pediatric Oncology, Hematology and Clinical Immunology, Medical Faculty, University Children's Hospital, Heinrich-Heine-University, Düsseldorf, Germany.
Manfred HönigDepartment of Pediatrics, University Medical Center Ulm, Ulm, Germany.
Ansgar SchulzDepartment of Pediatrics, University Medical Center Ulm, Ulm, Germany.
Sandra SteinmannDepartment of Pediatrics, University Medical Center Ulm, Ulm, Germany.
Klaus SchwarzInstitute for Clinical Transfusion Medicine and Immunogenetics Ulm, German Red Cross Blood Service Baden-Württemberg - Hessen and Institute for Transfusion Medicine, University Ulm, Ulm, Germany.
Gregor DückersCentre for Child and Adolescenct Health, Helios Klinikum Krefeld, Krefeld, Germany.
Beate LamersCentre for Child and Adolescenct Health, Helios Klinikum Krefeld, Krefeld, Germany.
Vanessa LangemeyerCentre for Child and Adolescenct Health, Helios Klinikum Krefeld, Krefeld, Germany.
Tim NiehuesCentre for Child and Adolescenct Health, Helios Klinikum Krefeld, Krefeld, Germany.
Sonu ShaiCentre for Child and Adolescenct Health, Helios Klinikum Krefeld, Krefeld, Germany.
Dagmar GrafMVZ Dr. Reising-Ackermann und Kollegen, Leipzig, Germany.
Carmen MüglichRheumatology/Clinical Immunology, Department of Internal Medicine II, University Hospital Würzburg, Würzburg, Germany.
Marc T SchmalzingRheumatology/Clinical Immunology, Department of Internal Medicine II, University Hospital Würzburg, Würzburg, Germany.
Eva C SchwaneckRheumatology/Clinical Immunology, Department of Internal Medicine II, University Hospital Würzburg, Würzburg, Germany.
Hans-Peter TonyRheumatology/Clinical Immunology, Department of Internal Medicine II, University Hospital Würzburg, Würzburg, Germany.
Johannes DirksPediatric Immunology, Department of Pediatrics, University Hospital Würzburg, Würzburg, Germany.
Gabriele HaasePediatric Immunology, Department of Pediatrics, University Hospital Würzburg, Würzburg, Germany.
Johannes G LiesePediatric Immunology, Department of Pediatrics, University Hospital Würzburg, Würzburg, Germany.
Henner MorbachPediatric Immunology, Department of Pediatrics, University Hospital Würzburg, Würzburg, Germany.
Dirk FoellDepartment of Pediatric Rheumatology and Immunology, University Children's Hospital, Muenster, Germany.
Antje HelligeDepartment of Pediatric Rheumatology and Immunology, University Children's Hospital, Muenster, Germany.
Helmut WittkowskiDepartment of Pediatric Rheumatology and Immunology, University Children's Hospital, Muenster, Germany.
Katja MasjosthusmannDepartment of General Pediatrics, University Children's Hospital Muenster, Muenster, Germany.
Michael MohrDepartment of Hematology, Oncology and Respiratory Medicine, University Hospital Muenster, Muenster, Germany.
Linda GeberzahnDepartment of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, Dresden, Germany.
Christian M HedrichDepartment of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, Dresden, Germany.
Christiane MüllerDepartment of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, Dresden, Germany.
Angela Rösen-WolffDepartment of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, Dresden, Germany.
Joachim RoeslerDepartment of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, Dresden, Germany.
Antje ZimmermannDepartment of Pediatrics, University Hospital Carl Gustav Carus, TU Dresden, Dresden, Germany.
Uta BehrendsDepartment of Pediatrics, Kinderklinik München Schwabing, StKM GmbH und Klinikum Rechts der Isar, Technische Universität München, Munich, Germany.
Nikolaus RieberDepartment of Pediatrics, Kinderklinik München Schwabing, StKM GmbH und Klinikum Rechts der Isar, Technische Universität München, Munich, Germany.
Uwe SchauerUniversity Children's Hospital, Ruhr University Bochum, Bochum, Germany.
Rupert HandgretingerDepartment of Oncology/Haematology, University Children's Hospital Tübingen, Tuebingen, Germany.
Ursula HolzerDepartment of Oncology/Haematology, University Children's Hospital Tübingen, Tuebingen, Germany.
Jörg HenesDepartment of Internal Medicine II (Oncology, Hematology, Rheumatology, Immunology), University Hospital Tübingen, Tuebingen, Germany.
Lothar KanzDepartment of Internal Medicine II (Oncology, Hematology, Rheumatology, Immunology), University Hospital Tübingen, Tuebingen, Germany.
Christoph BoeseckeDepartment of Internal Medicine I, Bonn University Hospital, Bonn, Germany.
Jürgen K RockstrohDepartment of Internal Medicine I, Bonn University Hospital, Bonn, Germany.
Carolynne Schwarze-ZanderDepartment of Internal Medicine I, Bonn University Hospital, Bonn, Germany.
Jan-Christian WasmuthDepartment of Internal Medicine I, Bonn University Hospital, Bonn, Germany.
Dagmar DillooDepartment of Paediatric Haematology and Oncology, Bonn University Hospital, Bonn, Germany.
Brigitte HülsmannDepartment of Paediatric Haematology and Oncology, Bonn University Hospital, Bonn, Germany.
Stefan SchönbergerDepartment of Paediatric Haematology and Oncology, Bonn University Hospital, Bonn, Germany.
Stefan SchreiberDepartment of General Internal Medicine, University Hospital Schleswig-Holstein, Kiel, Germany.
Rainald ZeunerDepartment of General Internal Medicine, University Hospital Schleswig-Holstein, Kiel, Germany.
Tobias AnkermannKlinik für Kinder und Jugendmedizin I, University Medical Center Schleswig-Holstein, Campus Kiel, Kiel, Germany.
Philipp von BismarckKlinik für Kinder und Jugendmedizin I, University Medical Center Schleswig-Holstein, Campus Kiel, Kiel, Germany.
Hans-Iko HuppertzProf.-Hess Childrens Hospital, Klinikum Bremen-Mitte, Bremen, Germany.
Petra Kaiser-LabuschProf.-Hess Childrens Hospital, Klinikum Bremen-Mitte, Bremen, Germany.
Johann GreilDepartment of Pediatric Oncology, Hematology and Immunology and Hopp Children's Tumor Center, University of Heidelberg, Heidelberg, Germany.
Donate JakobyDepartment of Pediatric Oncology, Hematology and Immunology and Hopp Children's Tumor Center, University of Heidelberg, Heidelberg, Germany.
Andreas E KulozikDepartment of Pediatric Oncology, Hematology and Immunology and Hopp Children's Tumor Center, University of Heidelberg, Heidelberg, Germany.
Markus MetzlerDivision of Pediatric Hematology and Oncology, Department of Pediatrics and Adolescent Medicine, University Hospital Erlangen, Erlangen, Germany.
Nora Naumann-BartschDivision of Pediatric Hematology and Oncology, Department of Pediatrics and Adolescent Medicine, University Hospital Erlangen, Erlangen, Germany.
Bettina SobikDivision of Pediatric Hematology and Oncology, Department of Pediatrics and Adolescent Medicine, University Hospital Erlangen, Erlangen, Germany.
Norbert GrafDepartment of Paediatric Haematology and Oncology, Saarland University Homburg, Homburg, Germany.
Sabine HeineDepartment of Paediatric Haematology and Oncology, Saarland University Homburg, Homburg, Germany.
Robin KobbeDivision for Pediatric Stem Cell Transplantation and Immunology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.
Kai LehmbergDivision for Pediatric Stem Cell Transplantation and Immunology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.
Ingo MüllerDivision for Pediatric Stem Cell Transplantation and Immunology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.
Friedrich HerrmannDepartment of Pediatrics, Asklepios Clinic Sankt Augustin, Sankt Augustin, Germany.
Gerd HorneffDepartment of Pediatrics, Asklepios Clinic Sankt Augustin, Sankt Augustin, Germany.
Ariane KleinDepartment of Pediatrics, Asklepios Clinic Sankt Augustin, Sankt Augustin, Germany.
Joachim PeitzDepartment of Pediatrics, Asklepios Clinic Sankt Augustin, Sankt Augustin, Germany.
Nadine SchmidtDepartment of Pediatrics, Asklepios Clinic Sankt Augustin, Sankt Augustin, Germany.
Stefan BielackPediatrics 5 (Oncology, Hematology, Immunology), Center for Pediatric, Adolescent and Women's Medicine, Klinikum Stuttgart - Olgahospital, Stuttgart, Germany.
Ute Groß-WieltschPediatrics 5 (Oncology, Hematology, Immunology), Center for Pediatric, Adolescent and Women's Medicine, Klinikum Stuttgart - Olgahospital, Stuttgart, Germany.
Carl F ClassenOncology Hematology Division, Department for Children and Adolescents, University Medicine Rostock, Rostock, Germany.
Jessica KlasenOncology Hematology Division, Department for Children and Adolescents, University Medicine Rostock, Rostock, Germany.
Peter DeutzRWTH University Hospital, Aachen, Germany.
Dirk KamitzRWTH University Hospital, Aachen, Germany.
Lisa LassayRWTH University Hospital, Aachen, Germany.
Klaus TenbrockRWTH University Hospital, Aachen, Germany.
Norbert WagnerRWTH University Hospital, Aachen, Germany.
Benedikt BernbeckClinic of Pediatrics, Klinikum Dortmund, Dortmund, Germany.
Bastian BrummelClinic of Pediatrics, Klinikum Dortmund, Dortmund, Germany.
Eusebia Lara-VillacanasClinic of Pediatrics, Klinikum Dortmund, Dortmund, Germany.
Esther MünstermannClinic of Pediatrics, Klinikum Dortmund, Dortmund, Germany.
Dominik T SchneiderClinic of Pediatrics, Klinikum Dortmund, Dortmund, Germany.
Nadine TietschClinic of Pediatrics, Klinikum Dortmund, Dortmund, Germany.
Marco WestkemperClinic of Pediatrics, Klinikum Dortmund, Dortmund, Germany.
Michael WeißDepartment of Pediatrics, Children's Hospital Amsterdamer Strasse, Cologne, Germany.
Christof KrammDivision of Pediatric Hematology and Oncology, University Medical Center Göttingen, Göttingen, Germany.
Ingrid KühnleDivision of Pediatric Hematology and Oncology, University Medical Center Göttingen, Göttingen, Germany.
Silke KullmannDivision of Pediatric Hematology and Oncology, University Medical Center Göttingen, Göttingen, Germany.
Hermann GirschickDepartment of Pediatrics, Vivantes Clinic, Berlin, Germany.
Christof SpeckerClinic of Rheumatology and Clinical Immunology, Hospitals Essen-Mitte, Essen, Germany.
Elisabeth Vinnemeier-LaubenthalClinic of Rheumatology and Clinical Immunology, Hospitals Essen-Mitte, Essen, Germany.
Henriette HaenickeDepartment of Pediatric and Adolescents Medicine, Helios Hospital Berlin-Buch, Berlin, Germany.
Claudia SchulzDepartment of Pediatric and Adolescents Medicine, Helios Hospital Berlin-Buch, Berlin, Germany.
Lothar SchweigererDepartment of Pediatric and Adolescents Medicine, Helios Hospital Berlin-Buch, Berlin, Germany.
Thomas G MüllerDepartment for Pediatrics I, Martin Luther University Hospital, Halle, Germany.
Martina StiefelDepartment for Pediatrics I, Martin Luther University Hospital, Halle, Germany.
Bernd H Belohradskydsai - Deutsche Selbsthilfe Angeborene Immundefekte e.V. (Patient Organization) e.V., Schnaitsee, Germany.
Veronika SoetedjoInstitute for Medical Biometry and Statistics, Faculty of Medicine and Medical Center, University of Freiburg, Freiburg, Germany.
Gerhard KindleInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Bodo GrimbacherInstitute for Immunodeficiency, Center for Chronic Immunodeficiency (CCI), Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

PubMed holds no abstract for this paper.

Indexed as

Immunologic Deficiency SyndromesAdolescentAdultAgedAged, 80 and overChildChild, PreschoolDelayed DiagnosisFemaleGenetic TherapyGermanyHematopoietic Stem Cell TransplantationHumansImmunoglobulinsInfantInfant, NewbornImmunoglobulinsCVIDEuropean Society for Immunodeficiencies (ESID)German PID-NET registryIgG substitution therapyPID prevalenceprimary immunodeficiency (PID)registry for primary immunodeficiency

Identifiers

PMID31379802
PMCPMC6659583

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