ReviewJournal of ultrasound2019
Congenital extrahepatic portosystemic shunt: description of four cases and review of the literature.
Review in Journal of ultrasound, 2019. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 13 papers.
What it found
Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.
The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.
The trial behind it
Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.
Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.
Who cites it
13 citing papers in PubMed, 26 citations in OpenAlex.
- Development of Hepatocellular Carcinoma in Type IB Abernethy Malformation.ACG case reports journal · 2026Article
- Type II Abernethy malformation presenting with heart failure: A case report.Radiology case reports · 2025Article
- Twelve-year review of galactosemia newborn screening in Taiwan: Evolving methods and insights.Molecular genetics and metabolism reports · 2024Article
- Percutaneous sequential closure of an Abernethy malformation: A case report.Radiology case reports · 2023Article
- Rare portal hypertension caused by Abernethy malformation (Type IIC): A case report.World journal of radiology · 2023Article
- Unexplained hyperammonemia and encephalopathy in the emergency department: Abernethy malformation in elderly patients.World journal of emergency medicine · 2023Article
- [Analysis of clinical features of 380 cases of special portal hypertension-Abernethy malformation].Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology · 2022Article
- Congenital Absence of the Portal Vein as a Rare Cause of Portopulmonary Hypertension-A Case Study Series.Medicina (Kaunas, Lithuania) · 2022Article
- A new variant of Abernethy malformation treated by transhepatic interventional closure: a case report.BMC gastroenterology · 2022Article
- Abernethy malformation: A comprehensive review.Diagnostic and interventional radiology (Ankara, Turkey) · 2022Review
- Abernethy syndrome in Slovenian children: Five case reports and review of literature.World journal of gastroenterology · 2020Review
- A basic understanding of congenital extrahepatic portosystemic shunt: incidence, mechanism, complications, diagnosis, and treatment.Intractable & rare diseases research · 2020Review
- Abernethy malformation and hepatocellular carcinoma: a serious consequence of a rare disease.BMJ case reports · 2020Article
Corrections and comments
PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.
Authors and funding
12 authors at 3 institutions in 1 country.
Funding
No grant is acknowledged in the PubMed record.
Abstract
Congenital extrahepatic portosystemic shunt (CEPS), also known as Abernethy malformation, is a rare condition in which the splenomesenteric blood drains directly into a systemic vein, bypassing the liver through a complete or partial shunt. The diagnosis is frequently made during childhood in the setting of neonatal cholestasis, hypergalactosemia, failure to thrive, mental retardation or other congenital defects. In adulthood, CEPS is usually found incidentally during diagnostic work-up for abdominal pain, liver test abnormalities, liver nodules, portopulmonary hypertension, portopulmonary syndrome or portosystemic encephalopathy. The diagnosis depends on imaging and portal venography, but sometimes only liver biopsy can be resolutive, demonstrating the absence of venules within the portal areas. Here we report four recent cases of Abernethy malformation diagnosed in young adults, in which ultrasound (US) was the initial imaging technique and allowed to suspect the diagnosis. Furthermore, we reviewed clinical presentations, associated anomalies and treatment of the 310 cases of CEPS previously reported in the literature.
Indexed as
Identifiers
What OpenQuestion holds
Registered trials
Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.