ReviewClinical ophthalmology (Auckland, N.Z.)2016
Ocular manifestations of Sturge-Weber syndrome: pathogenesis, diagnosis, and management.
Review in Clinical ophthalmology (Auckland, N.Z.), 2016. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 36 papers, 1 of them a synthesis that pooled it.
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Who cites it
36 citing papers in PubMed, 1 synthesis or guideline pooled it, 83 citations in OpenAlex.
- Pathophysiology, diagnosis, and management of glaucoma associated with Sturge-Weber syndrome.International ophthalmology · 2018Pooled it
- Salvage of a severed Paul Glaucoma Implant tube via anastomosis with an Ahmed Glaucoma Valve in a child with Sturge-Weber syndrome and complicated glaucoma: a case report.International journal of surgery case reports · 2026Article
- Preclinical Evaluation of Safety and Efficacy of QLS-111: A Novel Formulation of an Adenosine Triphosphate-Sensitive Potassium Channel Opener.Ophthalmology science · 2026Article
- A Case of Refractory Childhood Glaucoma Associated With Sturge-Weber Syndrome Treated With Baerveldt Glaucoma Implant.Case reports in ophthalmological medicine · 2026Article
- A Rare Case of Coexistence: Discoid Lupus Erythematosus and Sturge-Weber Syndrome.Clinical case reports · 2025Article
- New Trigger for Stroke-like Episode in Sturge-Weber Syndrome: A Case Report.Children (Basel, Switzerland) · 2025Article
- Sturge-Weber syndrome secondary glaucoma: From Pathogenesis to Treatment.Eye and vision (London, England) · 2025Review
- Multidisciplinary, multicenter consensus for the care of patients affected with Sturge-Weber syndrome.Orphanet journal of rare diseases · 2025Article
- Case Report: management of refractory glaucoma secondary to Sturge-Weber syndrome associated with ocular melanocytosis.Frontiers in medicine · 2025Article
- Resolution of exudative retinal detachment and optic disc edema in a child with Sturge Weber syndrome and congenital cyanotic heart disease after cardiac surgery.American journal of ophthalmology case reports · 2024Article
- Undiagnosed Epileptic Case Since Childhood of Sturge-Weber Syndrome: First Case Report from Somalia.International medical case reports journal · 2024Article
- Sturge-Weber syndrome: Updates in pathogenesis, diagnosis, and treatment.Annals of the Child Neurology Society · 2023Review
- Outcomes of Deep Sclerectomy for Glaucoma Secondary to Sturge-Weber Syndrome.Journal of clinical medicine · 2023Article
- Sturge-Weber Syndrome: A Review of Pathophysiology, Genetics, Clinical Features, and Current Management Approache.The application of clinical genetics · 2023Review
- Long-term outcomes in Primary congenital glaucoma, aniridia and anterior segment dysgenesis.European journal of ophthalmology · 2022Article
- Article
- EndothelialArteriosclerosis, thrombosis, and vascular biology · 2022Article
- Consensus Statement for the Management and Treatment of Sturge-Weber Syndrome: Neurology, Neuroimaging, and Ophthalmology Recommendations.Pediatric neurology · 2021Article
- Incidence of Sturge-Weber syndrome and associated ocular involvement in Olmsted County, Minnesota, United States.Ophthalmic genetics · 2020Article
- Vascular lesions of the head and neck: an update on classification and imaging review.Insights into imaging · 2020Review
Corrections and comments
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Authors and funding
5 authors at 2 institutions in 2 countries.
Funding
No grant is acknowledged in the PubMed record.
Abstract
Sturge-Weber syndrome has been included in the group of phakomatoses that is characterized by hamartomas involving the brain, skin, and eyes. The characteristic facial port-wine stain, involving the first branch of the trigeminal nerve and the embryonic vasculature distribution in this area, leads to several ocular complications of the anterior segment and can involve the eyelids and conjunctiva. The posterior segment of the eyes is also affected with diffuse choroidal hemangiomas. However, the most frequent ocular comorbidity is glaucoma with a prevalence rate ranging from 30%-70%. Glaucoma is related to anterior chamber malformations, high episcleral venous pressure (EVP), and changes in ocular hemodynamics. Glaucoma can be diagnosed at birth, but the disease can also develop during childhood and in adults. The management of glaucoma in Sturge-Weber syndrome patients is particularly challenging because of early onset, frequently associated severe visual field impairment at the time of diagnosis, and unresponsiveness to standard treatment. Several surgical approaches have been proposed, but long-term prognosis for both intraocular pressure control and visual function remains unsatisfactory in these patients. Choroidal hemangiomas may also lead to visual impairment thorough exudative retinal detachment and macular edema. Treatment of exudative hemangioma complications is aimed at destructing the tumor or decreasing tumor leakage.
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