ReviewJournal of cutaneous pathology2011
Erdheim-Chester disease presenting with cutaneous involvement: a case report and literature review.
Review in Journal of cutaneous pathology, 2011. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 11 papers.
What it found
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The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.
The trial behind it
Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.
Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.
Who cites it
11 citing papers in PubMed, 44 citations in OpenAlex.
- Single-Site ALK-Positive Histiocytosis With TFG-ALK Fusion: Expanding the Clinical Spectrum of This Rare Entity.The American journal of case reports · 2026Article
- Clinical presentation, imaging and response to interferon-alpha therapy in Erdheim-Chester disease: case-based review.Rheumatology international · 2020Review
- Erdheim-Chester Disease: A Case Report and Review of the Literature.Journal of clinical imaging science · 2020Article
- Case of Erdheim-Chester presenting with xanthelasma-like eruption and osteolytic bone lesions: A case report.SAGE open medical case reports · 2019Article
- Erdheim Chester disease in a patient with Burkitt lymphoma: a case report and review of literature.Diagnostic pathology · 2018Review
- Erdheim-Chester Disease Involving the Central Nervous System with the Unique Appearance of a Coated Vertebral Artery.NMC case report journal · 2016Article
- Erdheim-Chester disease (ECD): Case report, clinical and basic investigations, and review of literature.Medicine · 2016Review
- Diverse cutaneous manifestations of Erdheim-Chester disease in a woman with a history of Langerhans cell histiocytosis.JAAD case reports · 2016Article
- Multisystem Radiologic Manifestations of Erdheim-Chester Disease.Case reports in radiology · 2016Article
- Clinical considerations and key issues in the management of patients with Erdheim-Chester Disease: a seven case series.BMC medicine · 2014Article
- Erdheim-Chester Disease: a comprehensive review of the literature.Orphanet journal of rare diseases · 2013Review
Corrections and comments
PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.
Authors and funding
7 authors at 3 institutions in 1 country.
Funding
Abstract
Erdheim-Chester disease (ECD) is a rare, systemic, non-familial histiocytic disorder, first described by Jakob Erdheim and William Chester in 1930. Most patients have multiple sites of involvement at presentation. The most common site of involvement is the long bones of the axial skeleton, which is seen almost universally, followed by the nervous system, heart, lungs, orbit and retroperitoneum, which are seen in up to 50% of cases. Cutaneous involvement is rarely a presenting symptom of ECD, with two reported cases in the English literature. The diagnosis of ECD is rarely made by skin biopsy because of the relative rarity of cutaneous involvement as a presenting feature, and also perhaps because of the difficulty in distinguishing the histopathological appearance from potential mimics. The importance of distinguishing ECD from other cutaneous disorders with similar pathology lies in the implications for both treatment and prognosis. ECD is an aggressive, often fatal disorder, with death from disease occurring in greater than 50% of patients.
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Registered trials
Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.