ReviewWorld journal of gastroenterology2010
Experience of a single center with congenital hepatic fibrosis: a review of the literature.
Review in World journal of gastroenterology, 2010. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 32 papers.
What it found
Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.
The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.
The trial behind it
Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.
Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.
Who cites it
32 citing papers in PubMed, 90 citations in OpenAlex.
- Heritable Chronic Cholestatic Liver Diseases: A Review.Journal of clinical and translational hepatology · 2024Review
- [A case of cholangitis-type congenital hepatic fibrosis due to a mutation in the polycystic kidney/hepatic disease 1 gene].Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology · 2024Article
- [A case of neonatal liver failure].Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics · 2024Article
- Elderly onset congenital hepatic fibrosis with portal hypertension diagnosed after recurrent cholangitis: a case report.Clinical journal of gastroenterology · 2022Article
- Pediatric non-cirrhotic portal hypertension: Endoscopic outcome and perspectives from developing nations.World journal of hepatology · 2021Review
- Congenital hepatic fibrosis and its mimics: a clinicopathologic study of 19 cases at a single institution.Diagnostic pathology · 2021Article
- Congenital hepatic fibrosis in a young boy with congenital hypothyroidism: A case report.World journal of clinical cases · 2021Article
- Congenital hepatic fibrosis: case report and review of literature.The Pan African medical journal · 2021Review
- Factors contributing to diagnostic delay of Caroli syndrome: a single-center, retrospective study.BMC gastroenterology · 2020Article
- Morphometric changes and imaging findings of diffuse liver disease in relation to intrahepatic hemodynamics.Japanese journal of radiology · 2020Review
- Article
- Congenital Hepatic Fibrosis in Children and Adults: Clinical Manifestations, Management, and Outcome-Case Series and Literature Review.Gastroenterology research and practice · 2020Article
- Congenital hepatic fibrosis and coexistent retinal macular degeneration: A case report.Medicine · 2019Article
- The successful treatment of hepatocellular carcinoma arising from congenital hepatic fibrosis using radiofrequency ablation under laparoscopy.Clinical journal of gastroenterology · 2019Article
- Goldston syndrome with congenital hepatic fibrosis: A rare cause of neonatal cholestasis.Intractable & rare diseases research · 2019Article
- Article
- Transient Elastography for Detection of Liver Fibrosis in Children With Autosomal Recessive Polycystic Kidney Disease.Frontiers in pediatrics · 2018Article
- Congenital hepatic fibrosis in a 9-year-old female patient - a case report.Clinical and experimental hepatology · 2017Article
- Ultrasound of congenital and inherited disorders of the pediatric hepatobiliary system, pancreas and spleen.Pediatric radiology · 2017Review
- The emerging role of mast cells in liver disease.American journal of physiology. Gastrointestinal and liver physiology · 2017Review
Corrections and comments
PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.
Authors and funding
2 authors at 1 institution in 1 country.
Funding
No grant is acknowledged in the PubMed record.
Abstract
Congenital hepatic fibrosis (CHF) is an autosomal recessive inherited malformation defined pathologically by a variable degree of periportal fibrosis and irregularly shaped proliferating bile ducts. It is one of the fibropolycystic diseases, which also include Caroli disease, autosomal dominant polycystic kidney disease, and autosomal recessive polycystic kidney disease. Clinically it is characterized by hepatic fibrosis, portal hypertension, and renal cystic disease. CHF is known to occur in association with a range of both inherited and non-inherited disorders, with multiorgan involvement, as a result of ductal plate malformation. Because of the similarities in the clinical picture, it is necessary to differentiate CHF from idiopathic portal hypertension and early liver cirrhosis, for which a liver biopsy is essential. Radiological tests are important for recognizing involvement of other organ systems. With regards to our experience at Hacettepe University, a total of 26 patients have been diagnosed and followed-up between 1974 and 2009 with a diagnosis of CHF. Presentation with Caroli syndrome was the most common diagnosis, with all such patients presenting with symptoms of recurrent cholangitis and symptoms related to portal hypertension. Although portal fibrosis is known to contribute to the ensuing portal hypertension, it is our belief that portal vein cavernous transformation also plays an important role in its pathogenesis. In all patients with CHF portal vein morphology should be evaluated by all means since portal vein involvement results in more severe and complicated portal hypertension. Other associations include the Joubert and Bardet-Biedl syndromes.
Indexed as
Identifiers
What OpenQuestion holds
Registered trials
Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.