ReviewPediatric radiology2009
Fibropolycystic liver disease in children.
Review in Pediatric radiology, 2009. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 25 papers.
What it found
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The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.
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Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.
Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.
Who cites it
25 citing papers in PubMed.
- [A case of congenital hepatic fibrosis accompanied with multiple system abnormalities].Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology · 2025Article
- Prenatal diagnosis and molecular characterization ofFrontiers in genetics · 2025Article
- [A case of neonatal liver failure].Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics · 2024Article
- Diffusion tensor magnetic resonance imaging in the grading of liver fibrosis associated with congenital ductal plate malformations.Polish journal of radiology · 2023Article
- Dysregulation of the Scribble/YAP/β-catenin axis sustains the fibroinflammatory response in a PKHD1FASEB journal : official publication of the Federation of American Societies for Experimental Biology · 2022Article
- Hilar Fibropolycystic Liver Disease of Unknown Etiology: A Revelation from the Explant Liver.Journal of pediatric genetics · 2022Article
- Imaging analysis of the malignant transformation of bile duct hamartomas in the liver: A case report and literature review.Experimental and therapeutic medicine · 2022Article
- Hepatic manifestations of systemic disease: an imaging-based review.Pediatric radiology · 2022Review
- Inflammatory pathways and cholangiocarcinoma risk mechanisms and prevention.Advances in cancer research · 2022Review
- [A case of Caroli's disease confirmed by pathology, atypical symptoms and images].Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology · 2021Article
- Caroli's Syndrome: An Early Presentation.Cureus · 2020Article
- Pathobiology of inherited biliary diseases: a roadmap to understand acquired liver diseases.Nature reviews. Gastroenterology & hepatology · 2019Review
- The successful treatment of hepatocellular carcinoma arising from congenital hepatic fibrosis using radiofrequency ablation under laparoscopy.Clinical journal of gastroenterology · 2019Article
- Anaesthetic management of a child with Caroli's disease presenting for incidental surgery: A case report.Indian journal of anaesthesia · 2018Article
- Abernethy malformation associated with Caroli's syndrome in a patient with a PKHD1 mutation: a case report.Diagnostic pathology · 2017Article
- Ultrasound of congenital and inherited disorders of the pediatric hepatobiliary system, pancreas and spleen.Pediatric radiology · 2017Review
- [Clinical features of different clinical forms of childhood congenital hepatic fibrosis].Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics · 2016Article
- Stroke after percutaneous transhepatic variceal obliteration of esophageal varix in Caroli syndrome.Korean journal of pediatrics · 2013Article
- Boy with autosomal recessive polycystic kidney and autosomal dominant polycystic liver disease.Pediatric nephrology (Berlin, Germany) · 2012Article
- Molecular mechanisms of bile duct development.The international journal of biochemistry & cell biology · 2011Review
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Authors and funding
7 authors.
Funding
No grant is acknowledged in the PubMed record.
Abstract
Fibropolycystic liver diseases are a group of associated congenital disorders that present most often in childhood. These disorders include congenital hepatic fibrosis, biliary hamartomas, autosomal dominant polycystic liver disease, choledochal cysts and Caroli disease. We present a discussion and illustrations of the embryology, genetics, anatomy, pathology, imaging approach and key imaging features that distinguish fibropolycystic liver disease in children. The pathogenesis of these disorders is believed to be abnormal development of the embryonic ductal plates, which ultimately form the liver and biliary systems. An understanding of the abnormal embryogenesis helps to explain the characteristic imaging features of these disorders.
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Registered trials
Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the OpenQuestion graph.